Sprengel Deformity
FIGURE 19-1 Frontal plain radiograph demonstrating a right Sprengel deformity. CLINICAL QUESTIONS What is Sprengel deformity? What are the associated conditions? How is Sprengel deformity classified? What are the surgical…
Thumb Hypoplasia
FIGURE 10-1 Clinical photograph of a Blauth type IIIA hypoplastic thumb. Note lack of IP joint skin crease and thenar muscle bulk. CLINICAL QUESTIONS What are the characteristic clinical features…
Aphalangia and Amniotic Band Syndrome
FIGURE 9-1 Clinical photograph of a hand with amniotic band syndrome. Arrow points to the second web-space sinus tract with distal syndactyly. Congenital amputation and constriction band noted on third…
Radial Longitudinal Deficiency
FIGURE 13-1 Clinical photograph of radial longitudinal deficiency with a rudimentary pouce flottant. Evaluation of the radial deficiency starts at the chest wall and shoulder. Entire upper limb involvement does…
Pollicization
FIGURE 11-1 A: Clinical photograph of pouce flottant. B: Radiograph of same patient without proximal metacarpal, no CMC joint. This was treated with a pollicization. CLINICAL QUESTIONS What systemic conditions…
Macrodactyly
FIGURE 7-1 Macrodactyly of both the long and, less so, the index finger with divergence of the digits. An MRI of this patient revealed lipofibromatosis of the median nerve at…
Trigger Digits
FIGURE 12-1 Surgical technique of trigger thumb release. A: Clinical photograph of a pediatric trigger thumb. B: Prior to surgical release, marks are made on either side of the palpable…
Central Polydactyly
FIGURE 5-1 Photograph of father with untreated central synpolydactyly. CLINICAL QUESTIONS Under which category is central polydactyly classified? What are the genetics of this malformation? Are there associated syndromes or…
