Many of these cases however go unnoticed or discovered at autopsy.

In the pediatric age group, these patients commonly present with a scrotal swelling and may rarely present with an acute scrotal pain as a result of torsion or involvement of splenic tissue with other pathological conditions such as mumps, malaria, leukemia, trauma, and infectious mononucleosis.

The left side is far more commonly affected than the right in 98 % of the cases.

It is more common in males with an M to F ratio of 16:1.

This however may not be true as the ovary is not easily accessible and since the majority of these cases are asymptomatic, the incidence of splenogonadal fusion in females may be underestimated.