Rhabdomyosarcoma

Stage

Sites

Size

Orbit, non-parameningeal head and neck, non-bladder/prostate GU, biliary tract

T₁ or T₂

a or b

N₀, N₁, or N_x

Parameningeal, bladder/prostate, extremity, other

T₁ or T₂

N₀ or N_x

Parameningeal, bladder/prostate, extremity, other

T₁ or T₂

N₁

N₀, N₁, or N_x

All with distant metastases

T₁ or T₂

a or b

N₀ or N₁

Definitions: T = tumor invasiveness; T₁ = confined to anatomic site of origin; T₂ = extension and/or fixation to surrounding tissue; a = <5 cm; b = >5 cm; N = regional nodes; N₀ = regional nodes not clinically involved; N₁ = regional nodes clinically involved; N_x= clinical status of regional nodes unknown

(i)

Prognosis:

(i)

Stage/group/extent of disease; important predictor of outcome.

(ii)

Primary site; affects time to diagnosis, likelihood of lymphatic spread, ease of excision, and potentially radiation delivery; represents an important prognostic factor (favorable sites; orbit, non-bladder prostate GU, non-parameningeal head and neck, biliary tract).

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