Rhabdomyosarcoma


Stage

Sites

T

Size

N

1

Orbit, non-parameningeal head and neck, non-bladder/prostate GU, biliary tract

T1 or T2

a or b

N0, N1, or Nx

2

Parameningeal, bladder/prostate, extremity, other

T1 or T2

a

N0 or Nx

3

Parameningeal, bladder/prostate, extremity, other

T1 or T2

a

b

N1

N0, N1, or Nx

4

All with distant metastases

T1 or T2

a or b

N0 or N1


Definitions: T = tumor invasiveness; T1 = confined to anatomic site of origin; T2 = extension and/or fixation to surrounding tissue; a = <5 cm; b = >5 cm; N = regional nodes; N0 = regional nodes not clinically involved; N1 = regional nodes clinically involved; Nx= clinical status of regional nodes unknown




 


(i)

Prognosis:

(i)

Stage/group/extent of disease; important predictor of outcome.

 

(ii)

Primary site; affects time to diagnosis, likelihood of lymphatic spread, ease of excision, and potentially radiation delivery; represents an important prognostic factor (favorable sites; orbit, non-bladder prostate GU, non-parameningeal head and neck, biliary tract).

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Jan 7, 2017 | Posted by in PEDIATRICS | Comments Off on Rhabdomyosarcoma

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