Hirschsprung Disease: Soave (Open and Laparoscopic-Assisted) and Duhamel Techniques

CHAPTER 19 Hirschsprung Disease


Soave (Open and Laparoscopic-Assisted) and Duhamel Techniques




Open Endorectal (Soave) Pull-Through



Step 1: Surgical Anatomy








Step 3: Operative Steps





Leveling



The classic appearance of the proximal (ganglionic) bowel shows an extremely hypertrophied muscular wall, with a loss of the taenia coli (Fig. 19-2). The transition zone between aganglionic and ganglionic bowel can be made by a combination of visual inspection and a series of frozen sections. Once the presence of normal ganglion cells is identified, the bowel should be transected with a stapling device above the transition zone (ideally about 5 cm proximal or cranial to this point). This step is recommended because the level of aganglionosis can vary around the circumference of the colon, and proceeding more proximally will help to ensure that the selected bowel will have essentially normal pathology throughout. Both the proximal bowel and distal bowel are then mobilized, with the latter dissected to around 2 to 4 cm above the peritoneal reflection. Traction sutures are then placed at the end of the proximal colonic segment to facilitate the pull-through.



Endorectal Dissection




Once established, this plane of dissection is continued distally. Upward pulling on the traction sutures of the distal rectum is necessary to provide helpful countertraction. A helpful addition is the placement of other traction sutures into each quadrant of the muscle cuff as the dissection progressively develops (Fig. 19-4). Without the application of this countertraction, the dissection becomes ineffective, and one cannot proceed distally to an adequate level. Electrocautery should be used to coagulate larger communicating vessels between the submucosa and muscular cuff. The dissection should be carried out to within 0.5 cm of the dentate line in neonates and approximately 1 cm in older children.




Jun 18, 2016 | Posted by in PEDIATRICS | Comments Off on Hirschsprung Disease: Soave (Open and Laparoscopic-Assisted) and Duhamel Techniques

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