Fig. 1
Types of choledochal cyst. Type I: fusiform dilation of the common bile duct. Type II: saccular diverticulum of the common bile duct. Type III: choledochocele within wall of duodenum. Type IV: intrahepatic and extrahepatic biliary dilation, Type V: intrahepatic biliary dilation. CHD common hepatic duct, LHD left hepatic duct, RHD right hepatic duct. 1 Gallbladder, 2 Choledochal cyst (Source: Drriad, Creative Commons Attribution-Share Alike 3.0 Unported License via https://en.wikipedia.org/wiki/File:Choledochal_cysts.svg. Downloaded 23 Dec 2013)
(i)
Type I: Cystic dilation of the common bile duct (fusiform) 90 %.
(ii)
Type II: Diverticular malformation of the common bile duct (saccular).
(iii)
Type III: Choledochocele within the wall of the duodenum.
(iv)
Type IV: Intrahepatic and extrahepatic multiple cysts.
(v)
Type V: Multiple intrahepatic cysts.
(vi)
Type VI: Rare variant – cystic dilation of cystic duct.
(vii)
Caroli disease:
1.
Caroli disease is multiple intrahepatic cysts associated with hepatic fibrosis.
2.
Cysts in Caroli disease are bile collections that do not communicate with biliary tree.
(d)
Risk of malignancy if left untreated.
2.
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Clinical presentation:
(a)
Prenatal diagnosis with sonography: has become a more common mode of presentation.
(b)
Newborns: present with obstructive jaundice.
(c)
Infants: present with abdominal pain, abdominal mass, and jaundice.